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The International Pleuropulmonary Blastoma Registry
The International Pleuropulmonary Blastoma Registry
The Genetics of PPB

Critical Issues


Constitutional & Familial Issues: Genetics of PPB:


A Very Rare Disease: Enrolling Patients in the Registry


Cerebral Metastases in PPB


Genetic Study of PPB


PPB Associated with Cystic Nephroma and Other Renal Tumors


Type I PPB: Treatment Issues


Type II and III THERAPY RECOMMENDATION CHANGE

Join Our PPB Study

Whats New

04/09/2010
2010 PPB FAMILY WEEKEND IN WASHINGTON DC

02/15/2007
THERAPY CHANGE: PPB Types II and III

11/15/2006
PPB, Cystic Nephroma & Small Bowel Polyps

10/01/2005
Genetic Study in PPB - PPB Tissue Bank

Literature Sources
Please use the search field or click on a focus category to locate a specific literature source.
15 Search Results :
2009 Priest JR, Williams GM, Hill DA, Dehner LP, Jaffé A.
Pulmonary cysts in early childhood and the risk of malignancy.
Pediatr Pulmonol
44(1):14-30.
Number of Cases: 0
Focus Categories: Type I PPB  Registry publication  major review  lung cyst  imaging of PPB  familial/constitutional  cyst management 
2008 Herman TE, Siegel MJ
Neonatal pleuropulmonary blastoma, type 1.
J Perinatol
28(1):82-4.
Number of Cases: 1
Focus Categories: imaging of PPB  Type I PPB 
2008 Hill DA, Jarzembowski JA, Priest JR, Williams G, Schoettler P, Dehner LP.
Type I pleuropulmonary blastoma: pathology and biology study of 51 cases from the International Pleuropulmonary Blastoma Registry.
Am J Surg Pathol
32(2):282-295
Number of Cases: 51
Focus Categories: Type I PPB  Registry publication  pathology discussion 
2007 Shivastava R, Saha A, Mehera B, Batra P, Gagane NM.
Pleuropulmonary blastoma: transition from type I (cystic) to type III (solid).
Singapore Med J
48(7):e190-2.
Number of Cases: 1
Focus Categories: Type I PPB  type progression 
2007 Bradnock TJ, MacKinlay GA, McKenzie K.
Thoracoscopic lobectomy for symptomatic CCAM in a five month old infant: a cautionary tale from the patholgist [Abstract].
J Laparoendosc Adv Surg Tech
17:547.
Number of Cases: 1
Focus Categories: Type I PPB 
2007 Pai S, Eng HL, Lee SY, Hsaio CC, Huang WT, Huang SC, Hill DA, Dehner LP, Priest JR.
Correction: Pleuropulmonary blastoma, not rhabdomyosarcoma in a congenital lung cyst [Letter to the Editor].
Pediatr Blood Cancer
Mar;48(3):370-1.
Number of Cases: 1
Focus Categories: cyst management  lung cyst  pathology discussion  Registry publication  Type I PPB 
2007 David M, Bosdure E, deLagausie P, Rome A, Gorincour G, Chabrol B, Dubus JC.
Kystic pleuropulmonary blastoma fortuitly discovered in an infant.
Arch Pediatr
Oct 10:Epub
Number of Cases: 1
Focus Categories: Type I PPB 
2007 Belcher E, Lawson MH, Nicholson AG, Davison A, Goldstraw P.
Congenital cystic adenomatoid malformation presenting as in-flight systemic air embolisation.
Eur Respir J
30:801-4.
Number of Cases: 1
Focus Categories: Type I PPB 
2006 Park II, Lee EB.
Pleuropulmonary blastoma in lung.
Korean J Thorac Cardiovasc Surg
39(9):722-24.
Number of Cases: 1
Focus Categories: imaging of PPB  pathology discussion  Type I PPB 
2006 Priest JR, Hill DA, Williams GM, Moertel CM, Messinger Y, Finkelstein MJ, Dehner LP.
Type I pleuropulmonary blastoma: A report from the International Pleuropulmonary Blastoma Registry.
J Clin Oncol
24:4492-8.
Number of Cases: 38
Focus Categories: Type I PPB  Registry publication  major review  cyst management 
2006 Miniati DN, Chintagumpala M, Langston C, Dishop MK, Olutoye OO, Nuchtern JG, Cass DL.
Prenatal presentation and outcome of children with pleuropulmonary blastoma.
J Pediatr Surg
41:66-71.
Number of Cases: 10
Focus Categories: bilateral  lung cyst  cyst management  Type I PPB 
2006 Vargas SO, Korpershoek E, Kozakewich HP, Krijger RR, Fletcher JA, Perez-Atayde AR.
Cytogenetic and p53 profiles in congenital cystic adenomatoid malformation: insights into its relationship with pleuropulmonary blastoma.
Pediatr Dev Pathol
9(3):190-5.
Number of Cases: 2
Focus Categories: Type I PPB  pathology discussion  molecular studies 
2005 Priest JR, Messinger Y, Finkelstein MJ, Williams GM, Hill DA, Dehner LP, Moertel CL.
Treatment modality vs outcome in Type I pleuropulmonary blastoma (PPB) - Results from The PPB Registry [abstract].
Pediatr Blood Cancer
44(6):544
Number of Cases: 33
Focus Categories: Registry publication  Type I PPB 
2004 Ozer E, Sanli A, Erbayraktar S, Ulukus C, Onen A.
Congenital cystic adenomatoid malformation type 4 and aneurysm of the vein of galen: a rare coincidence or possibly related association.
Pediatr Dev Pathol
7:268-272.
Number of Cases: 1
Focus Categories: Type I PPB  familial/constitutional 
2000 Chan JK.
Pleuropulmonary blastoma type I, specimen partially deroofed and photographed under water.
Int J Surg Pathol
8(3):240
Number of Cases: 1
Focus Categories: Type I PPB 

Keyword Search:



Focus Categories:

adult
ASCR - PBSCT
bilateral
CNS metastasis
cyst management
cystic nephroma
cytogenetics
DICER1 mutation
familial/constitutional
fine needle aspiration
general PPB-related topic
imaging of PPB
lung cyst
macrovascular invasion/embolism
major review
molecular studies
neo-adjuvant chemotherapy
pathology discussion
Registry publication
survival of CNS metastasis
SVC syndrome
Type I PPB
type progression


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Data and recommendations on this site are conscientiously presented but some are unpublished observations and have not undergone peer review. Consultation with the Registry is encouraged to clarify any topics. The International PPB Registry advises caution in the citation of website information.
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