2010	Hill DA, Wang JD, Schoettler P, Dehner L, Ivanovich J, Bracamontes D, Williams G, Messinger Y, Goodfellow PJ, Priest J. Germline DICER1 mutations are common in both hereditary and presumed sporadic pleuropulmonary blastoma [Abstract]. Lab Invest 90:311 Number of Cases: 68 Focus Categories: Registry publication  familial/constitutional  DICER1 mutation
2010	Cummings NM, Desai S, Thway K, Stewart S, Hill DA, Priest JR, Nicholson AG, Rintoul RC. Cystic primary pulmonary synovial sarcoma presenting as recurrent pneumothorax: report of four cases. Am J Surg Pathol 34(8):1176-79. Number of Cases: 4 Focus Categories: Registry publication  adult
2010	Priest JR, Jaffe A. Increasing incidence of detection of congenital lung lesions [Reply]. Pediatr Pulmonol 45:104. Number of Cases: 0 Focus Categories: lung cyst  Registry publication
2010	Schultz KA, Williams G, Hill D, Dehner LP, Priest J. Ovarian tumors in association with pleuropulmonary blastoma: a new manifestation of the PPB Tumor syndrome [Abstract]. Pediatr Blood Cancer 54(6):850 Number of Cases: 8 Focus Categories: Registry publication  familial/constitutional
2010	Priest JR, Williams GM, Mize WA, Dehner LP. Priest JR, Williams GM, Mize WA, Dehner LP. Nasal chondromesenchymal hamartoma in children with pleuropulmonary blastoma: a report from the International Pleuropulmonary Blastoma Registry. Int J Pediatr Otorhinolaryngol [in press] Number of Cases: 4 Focus Categories: familial/constitutional  Registry publication
2010	Cross SF, Arbuckle S, Priest JR, Marshall G, Charles A, Dalla Pozza, L. Familial Pleuropulmonary Blastoma in Australia Pediatric Blood and Cancer in press Number of Cases: 4 Focus Categories: Registry publication  familial/constitutional  cystic nephroma
2010	Priest JR, Andic D, Arbuckle S, Gonzalez-Gomez I, Hill DA Williams G. Great vessel and cardiac extension and tumor embolism in pleuropulmonary blastoma - a report from the International Pleuropulmonary Blastoma Registry Pediatric Blood and Cancer in press Number of Cases: 11 Focus Categories: imaging of PPB  macrovascular invasion/embolism  neo-adjuvant chemotherapy  Registry publication  SVC syndrome
2009	Dehner LP. USCAP Specialty Conference, case 4: Sertoli cell tumor of the ovary. Pediatr Dev Pathol In Press Number of Cases: 1 Focus Categories: familial/constitutional  pathology discussion  Registry publication
2009	Hill DA, Ivanovich J, Priest JR, Gurnett CA, Dehner LP, Desruisseau D, Jarzembowski JA, Wikenheiser-Brokamp KA, Suarez BK, Whelan AJ, Williams G, Bracamontes D, Messinger Y, Goodfellow PJ. DICER1 Mutations in Familial Pleuropulmonary Blastoma. Science 325:965 Number of Cases: 11 Focus Categories: Registry publication  molecular studies  major review  familial/constitutional  DICER1 mutation
2009	Schiavetti A, Indolfi P, Hill DA, Priest JR Primary pulmonary rhabdomyosarcoma in childhood: clinico-biologic features in two cases with review of the literature--erratum Pediatr Blood Cancer 52(1):146. Number of Cases: 2 Focus Categories: pathology discussion  Registry publication
2009	Priest JR, Williams GM, Hill DA, Dehner LP, Jaffé A. Pulmonary cysts in early childhood and the risk of malignancy. Pediatr Pulmonol 44(1):14-30. Number of Cases: 0 Focus Categories: Type I PPB  Registry publication  major review  lung cyst  imaging of PPB  familial/constitutional  cyst management
2009	Hill DA, Ivanovich J, Priest JR, Gurnett CA, Dehner LP, Desruisseau D, Jarzembowski JA, Wikenheiser KA, Suarez BK, Whelan AJ, Williams G, Bracamontes B, Messinger Y, Goodfellow PJ. Inherited DICER1 mutations in familial pleuropulmonary blastoma [abstract]. Annual Meeting for American Association for Cancer Research Abstract LB-91. Number of Cases: 11 Focus Categories: Registry publication  familial/constitutional  DICER1 mutation
2008	Hill DA, Jarzembowski JA, Priest JR, Williams G, Schoettler P, Dehner LP. Type I pleuropulmonary blastoma: pathology and biology study of 51 cases from the International Pleuropulmonary Blastoma Registry. Am J Surg Pathol 32(2):282-295 Number of Cases: 51 Focus Categories: Type I PPB  Registry publication  pathology discussion
2007	Hill DA, Jarzembowski JA, Lennerz JK, Spence D, Schoettler P, Priest JR, Williams G, Dehner LP. Histologic features of Type I pleuropulmonary blastoma (PPB) [Abstract]. Annual Meeting of the Society for Pediatric Pathology Mar. Number of Cases: 41 Focus Categories: pathology discussion  Registry publication
2007	Hill DA, Dishop MK, McKay EM, Langston C, Priest JR, Dehner LP. Immature interstitial mesenchymal tumor (IIMT): a distinctive new entity of the infant lung [Abstract]. Mod Pathol 20:279-300. Number of Cases: 4 Focus Categories: pathology discussion  Registry publication
2007	Priest JR, Magnuson J, Williams GM, Abromowitch M, Byrd R, Sprinz P, Finkelstein M, Moertel CL, Hill DA. Cerebral metastasis and other central nervous system complications of pleuropulmonary blastoma. Pediatr Blood Cancer 49(3):266-73. Number of Cases: 39 Focus Categories: Registry publication  major review  CNS metastasis
2007	Pai S, Eng HL, Lee SY, Hsaio CC, Huang WT, Huang SC, Hill DA, Dehner LP, Priest JR. Correction: Pleuropulmonary blastoma, not rhabdomyosarcoma in a congenital lung cyst [Letter to the Editor]. Pediatr Blood Cancer Mar;48(3):370-1. Number of Cases: 1 Focus Categories: cyst management  lung cyst  pathology discussion  Registry publication  Type I PPB
2007	Lennerz JK, Jarzembowski JA, Spence D, Schoettler P, Dehner LP, Hill DA. Diagnostic features of pleuropulmonary blastoma (PPB) are absent in congenital cystic adenomatoid malformation [Abstract]. Annual Meeting of the Society for Pediatric Pathology Mar. Number of Cases: 57 Focus Categories: pathology discussion  Registry publication
2006	Priest JR, Hill DA, Williams GM, Moertel CM, Messinger Y, Finkelstein MJ, Dehner LP. Type I pleuropulmonary blastoma: A report from the International Pleuropulmonary Blastoma Registry. J Clin Oncol 24:4492-8. Number of Cases: 38 Focus Categories: Type I PPB  Registry publication  major review  cyst management
2006	Stefanaki K, Boman F, Stassinopoulou A, Williams GM, Fournet JC, Bouron-Dal Soglio D, Chauvenet A, Hill A, Messinger Y, Priest JR. Association of pleuropulmonary blastoma with cystic nephroma and small bowel polyp: case report and data from the International Pleuropulmonary Blastoma Registry [Abstract]. Virchows Arch 448:692. Number of Cases: 2 Focus Categories: Registry publication  cystic nephroma
2006	Boman F, Hill DA, Williams GM, Chauvenet A, Fournet JC, BouronDalSoglio D, Messinger Y, Priest JR. Familial association of pleuropulmonary blastoma with cystic nephroma and other renal tumors: a report from the International Pleuropulmonary Blastoma Registry. J Pediatr 149(6):850-4.e2. Number of Cases: 18 Focus Categories: Registry publication  major review  familial/constitutional  cystic nephroma
2006	Hill DA, Williams GM, Finkelstein MJ, Serrano MF, Dehner LP, Priest JR. Significance of histologic type and anaplasia in pleuropulmonary blastoma [Abstract]. Lab Invest 86(Suppl):212-27. Number of Cases: 116 Focus Categories: pathology discussion  Registry publication
2005	Dehner LP. Beware of "degenerating" congenital pulmonary cysts [Letter to the Editor]. Pediatr Surg Int 21:123-4 Number of Cases: 4 Focus Categories: cyst management  cystic nephroma  pathology discussion  Registry publication
2005	Boman F, Hill DA, Williams GM, Bouron-Dal Soglio D, Fournet JC, Messinger Y, Priest JR. Association of pleuropulmonary blastoma with cystic nephroma and other renal lesions: cases from the International Pleuropulmonary Blastoma Registry [Abstract]. Annual Mtg Society for Pediatr Pathol 58:84. Number of Cases: 18 Focus Categories: Registry publication  cystic nephroma
2005	Serrano MF, Dehner LP, Williams GM, Priest JR, Hill DA. Histologic predictors of central nervous system metastasis in pleuropulmonary blastoma: a pilot study [Abstract]. Mod Pathol 18:303. Number of Cases: 35 Focus Categories: survival of CNS metastasis  Registry publication  pathology discussion  CNS metastasis
2005	Hill DA. USCAP Specialty Conference, case 1: Type I Pleuropulmonary blastoma. Pediatr Dev Pathol 8:77-84 Number of Cases: 1 Focus Categories: cystic nephroma  major review  pathology discussion  Registry publication
2005	Priest JR, Messinger Y, Finkelstein MJ, Williams GM, Hill DA, Dehner LP, Moertel CL. Treatment modality vs outcome in Type I pleuropulmonary blastoma (PPB) - Results from The PPB Registry [abstract]. Pediatr Blood Cancer 44(6):544 Number of Cases: 33 Focus Categories: Registry publication  Type I PPB
2004	Hill DA, Dehner LP. A cautionary note about congenital cystic adenomatoid malformation (CCAM) type 4 [Letter]. Am J Surg Pathol 28(4):554-5. Number of Cases: 0 Focus Categories: cyst management  lung cyst  pathology discussion  Registry publication
2004	Messinger YH, Dehner LP, Hill DA, Williams G, Priest JR. Pleuropulmonary blastoma and its association with other childhood neoplasms [abstract]. J Clin Oncol 22(14S):8542 Number of Cases: 82 Focus Categories: cystic nephroma  familial/constitutional  Registry publication
2004	Priest J, Watterson J, Dehner L, Friend S, McIntyre J, Strong L, Hansen M, Byrd B, Feusner J, Amylon M, Bostrom B, Langston C, Pappo A. Childhood pleuropulmonary blastoma (PPB) as a unique marker for familial childhood neoplasms [Abstract]. Proceedings of ASCO 13:186. Number of Cases: 12 Focus Categories: Registry publication  familial/constitutional  cytogenetics
2004	Priest J, Williams G. Incidence, timing, and outcome of central nervous system metastasis in pleuropulmonary blastoma [Abstract]. 11th International Symposium on Pediatric Neuro-Oncology EPI30:67. Number of Cases: 24 Focus Categories: CNS metastasis  Registry publication  survival of CNS metastasis
2004	Dehner LP, Tazelaar HD, Manabe T. Pleuropulmonary blastoma.In Travis WD, Brambilla E, Muller-Hermelink HK, Harris CC (eds): World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of the Lung, Pleura, Thymus and Heart. Lyon, IARC Press :99-100. Number of Cases: 0 Focus Categories: general PPB-related topic  pathology discussion  Registry publication
1999	Hill DA, Sadeghi S, Schultz MZ, Burr JS, Dehner LP. Pleuropulmonary blastoma in an adult. Cancer 85(11):2368-74. Number of Cases: 1 Focus Categories: adult  neo-adjuvant chemotherapy  Registry publication
1998	McDermott MB, Ponder TB, Dehner LP. Nasal chondromesenchymal hamartoma: an upper respiratory tract analogue of the chest wall mesenchymal hamartoma. Am J Surg Pathol 22(4):425-33. Number of Cases: 1 Focus Categories: Registry publication  pathology discussion  major review  general PPB-related topic
1997	Priest JR, McDermott MB, Bhatia S, Watterson J, Manivel JC, Dehner LP. Pleuropulmonary blastoma: a clinicopathologic study of 50 cases. Cancer 80(1):147-61. Number of Cases: 50 Focus Categories: Registry publication  major review  cyst management  bilateral
1996	McDermott MB, Dehner LP, Priest JR. Pleuropulmonary blastoma and congenital cystic malformations [Letter to the editor]. J Peds 129(5): 774-5. Number of Cases: 0 Focus Categories: cyst management  pathology discussion  Registry publication
1996	Priest JR, Watterson J, Strong L, Huff V, Woods WG, Byrd RL, Friend SH, Newsham I, Amylon MD, Pappo A, Mahoney DH, Langston C, Heyn R, Kohut G, Freyer DR, Bostrom B, Richardson MS, Barredo J, Dehner LP. Pleuropulmonary blastoma: a marker for familial disease. J Pediatr 128(2):220-4. Number of Cases: 12 Focus Categories: Registry publication  major review  familial/constitutional  cytogenetics  cystic nephroma
1995	Boyer MW, Moertel CL, Priest JR, Woods WG. Use of intracavitary cisplatin for the treatment of childhood solid tumors in the chest or abdominal cavity. J Clin Oncol 13(3):631-6. Number of Cases: 2 Focus Categories: Registry publication
1995	Dehner LP, Watterson J, Priest J. Pleuropulmonary blastoma. A unique intrathoracic-pulmonary neoplasm of childhood. Perspect Pediatr Pathol 18:214-26. Number of Cases: 38 Focus Categories: major review  pathology discussion  Registry publication
1994	Dehner LP. Pleuropulmonary blastoma is THE pulmonary blastoma of childhood. Semin Diagn Pathol 11(2):144-51. Number of Cases: 0 Focus Categories: major review  pathology discussion  Registry publication
1988	Manivel JC, Priest JR, Watterson J, Steiner M, Woods WG, Wick MR, Dehner LP. Pleuropulmonary blastoma. The so-called pulmonary blastoma of childhood. Cancer 62(8):1516-26. Number of Cases: 11 Focus Categories: major review  pathology discussion  Registry publication
1987	Allan BT, Day DL, Dehner LP. Primary pulmonary rhabdomyosarcoma of the lung in children. Report of two cases presenting with spontaneous pneumothorax. Cancer 59(5):1005-11. Number of Cases: 2 Focus Categories: lung cyst  Registry publication
1987	Manivel C, Wick M, Dehner L. Thoracopulmonary blastoma - reassessment of an embryonal neoplasm [Abstract]. Lab Invest 56:46A. Number of Cases: 9 Focus Categories: pathology discussion  Registry publication